choroideremia

choroideremia [kôr′oi-də-rē′mē-ə, kô-] n.

1. Congenital absence of the choroid of the eye.
2. The progressive degeneration of the choroid in males, beginning with peripheral pigmentary retinopathy, followed by atrophy of the retinal pigment epithelium and of the choriocapillaris, night blindness, progressive constriction of visual fields, and finally complete blindness.